Actualización en el diagnóstico y tratamiento de la Fibrosis Pulmonar Idiopática: Revisión Bibliográfica
Resumen
La fibrosis pulmonar idiopática (FPI) es una enfermedad crónica y progresiva de causa desconocida, generalmente asociada a un mal pronóstico, caracterizada por cambios morfológicos definitivos que alteran la arquitectura del parénquima pulmonar, como resultado final genera una fibrosis irreversible, insuficiencia respiratoria y finalmente la muerte. Actualmente han existido avances importantes para comprender la fisiopatología de la FPI, sin embargo, a pesar de los avances innegables, el diagnóstico de la FPI sigue siendo un reto; requiere de personal médico entrenado acompañado de una evaluación multidisciplinar para alcanzar un diagnóstico certero, efectivo e individualizado. La implementación de los fármacos antifibróticos crearon un mejor panorama para el tratamiento de la FPI y actualmente se están evaluando nuevos fármacos prometedores. Respondiendo a las necesidades de los pacientes se debe hacer énfasis en el tratamiento no farmacológico de la FPI, que permite reducir la sintomatología y mejorar la calidad de vida.
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Derechos de autor 2023 Oscar David Maliza Torres;Washington David Arias Calvache
Esta obra está bajo licencia internacional Creative Commons Reconocimiento 4.0.
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