Malformación Congénita De La Vía Aérea Pulmonar Del Adulto Asociada A Persistencia De Ductus Arterioso
Palabras clave:
malformación de la vía área pulmonar congénita, malformación adenomatoidea quística congénita, malformación congénita pulmonar
Resumen
La malformación de la vía área pulmonar congénita (MVAPC), previamente conocida como malformación adenomatoidea quística congénita (MAQC), es una anomalía rara en el desarrollo pulmonar, cuyo diagnóstico comúnmente se hace antes de los 2 años de vida, resultando excepcional en adultos. El presente caso hace referencia a una mujer adulta joven que tiene como antecedente infecciones respiratorias recurrentes, además de hallazgos imagenológicos sugerentes de cavidades quísticas y, concomitantemente se documenta la persistencia del conducto arterioso. El diagnóstico de esta patología requiere una acertada disertación clínica entorno a la sintomatología y signología manifestada por la paciente, para así poder llegar a la conducta quirúrgica y así mejorar sustancialmente su calidad de vida.
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https://pubs.rsna.org/doi/10.1148/radiographics.11.5.1947321
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https://pubmed.ncbi.nlm.nih.gov/27770196/
6. Pogoriler J, Swarr D, Kreiger P, Adzick NS, Peranteau W. Congenital Cystic Lung Lesions: Redefining the natural distribution of subtypes and assessing the risk of malignancy. Am J Surg Pathol [Internet]. 2019 Jan 1 [cited 2024 Jan 11];43(1):47. Available from: /pmc/articles/PMC6816050/
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8. Hermelijn SM, Zwartjes RR, Tiddens HAWM, Cochius-Den Otter SCM, Reiss IKM, Wijnen RMH, et al. Associated Anomalies in Congenital Lung Abnormalities: A 20-Year Experience. Neonatology [Internet]. 2020 Feb 1 [cited 2024 Jan 12];117(6):697–703. Available from: https://pubmed.ncbi.nlm.nih.gov/32841951/
9. Scamporlino A, Ambrosini A, Turrini E, Morandi U, Stefani A. Congenital cystic adenomatoid malformation in adults, presenting as a single cyst. https://doi.org/101177/0218492318776572 [Internet]. 2018 May 2 [cited 2024 Jan 12];26(5):407–9. Available from:
https://journals.sagepub.com/doi/10.1177/0218492318776572?url_ver=Z39.88-2003&rfr_id=ori%3Arid%3Acrossref.org&rfr_dat=cr_pub++0pubmed
10. Patz EF, Müller NL, Swensen SJ, Dodd LG. Congenital cystic adenomatoid malformation in adults: CT findings. J Comput Assist Tomogr [Internet]. 1995 [cited 2024 Jan 11];19(3):361–4. Available from:
https://pubmed.ncbi.nlm.nih.gov/7790542/
11. Zeng Z, Liu C, Liu C, Pu Q, Mei J, Liao H, et al. Clinical characteristics and surgical treatment of congenital cystic adenomatoid malformation in adults: the largest cohort of 46 patients. Ann Transl Med [Internet]. 2022 May [cited 2024 Jan 11];10(10):596–596. Available from:
https://pubmed.ncbi.nlm.nih.gov/35722391/
12. Hartman GE, Shochat SJ. Primary pulmonary neoplasms of childhood: a review. Ann Thorac Surg [Internet]. 1983 [cited 2024 Jan 12];36(1):108–19. Available from:
https://pubmed.ncbi.nlm.nih.gov/6344822/
13. K Y CH’IN, M Y TANG. Arch Pathol (Chic). Sep;48(3):221-9. 1949 [cited 2024 Jan 11]. Congenital adenomatoid malformation of one lobe of a lung with general anasarca. Available from:
https://pubmed.ncbi.nlm.nih.gov/18137795/
14. Stocker JT, Madewell JE, Drake RM. Congenital cystic adenomatoid malformation of the lung. Classification and morphologic spectrum. Hum Pathol [Internet]. 1977 [cited 2024 Jan 11];8(2):155–71. Available from:
https://pubmed.ncbi.nlm.nih.gov/856714/
15. Stocker J.T. Congenital pulmonary airway malformation : a new name and expanded classification of congenital cystic adenomatoid malformation of the lung. Histopathology [Internet]. 2002 [cited 2024 Jan 11];41(2):424–31. Available from:
https://cir.nii.ac.jp/crid/1574231874759255680
16. Scott Adzick N, Harrison MR, Glick PL, Golbus MS, Anderson RL, Mahony BS, et al. Fetal cystic adenomatoid malformation: prenatal diagnosis and natural history. J Pediatr Surg [Internet]. 1985 [cited 2024 Jan 12];20(5):483–8. Available from:
https://pubmed.ncbi.nlm.nih.gov/3903097/
17. Gorospe L, Muñoz-Molina GM, Ayala-Carbonero AM, Fernández-Méndez MÁ, Arribas-Marcos Á, Castro-Acosta P, et al. Cystic adenomatoid malformation of the lung in adult patients: clinicoradiological features and management. Clin Imaging [Internet]. 2016 May 1 [cited 2024 Jan 14];40(3):517–22. Available from: https://pubmed.ncbi.nlm.nih.gov/27133697/
2. Rosado-de-Christenson ML, Stocker JT. Congenital cystic adenomatoid malformation. https://doi.org/101148/radiographics1151947321 [Internet]. 1991 Sep 1 [cited 2024 Jan 11];11(5):865–86. Available from:
https://pubs.rsna.org/doi/10.1148/radiographics.11.5.1947321
3. Taylor B, Rice A, Nicholson AG, Hind M, Dean CH. Mechanism of lung development in the aetiology of adult congenital pulmonary airway malformations. Thorax [Internet]. 2020 Nov 1 [cited 2024 Jan 11];75(11):1001. Available from: /pmc/articles/PMC7569368/
4. Lezmi G, Hadchouel A, Khen-Dunlop N, Vibhushan S, Benachi A, Delacourt C. Malformations adénomatoïdes kystiques du poumon : diagnostic, prise en charge, hypothèses physiopathologiques. Rev Pneumol Clin. 2013 Aug 1;69(4):190–7.
5. Lau CT, Kan A, Shek N, Tam P, Wong KKY. Is congenital pulmonary airway malformation really a rare disease? Result of a prospective registry with universal antenatal screening program. Pediatr Surg Int [Internet]. 2017 Jan 1 [cited 2024 Jan 11];33(1):105–8. Available from:
https://pubmed.ncbi.nlm.nih.gov/27770196/
6. Pogoriler J, Swarr D, Kreiger P, Adzick NS, Peranteau W. Congenital Cystic Lung Lesions: Redefining the natural distribution of subtypes and assessing the risk of malignancy. Am J Surg Pathol [Internet]. 2019 Jan 1 [cited 2024 Jan 11];43(1):47. Available from: /pmc/articles/PMC6816050/
7. Kunisaki SM. Narrative review of congenital lung lesions. Transl Pediatr [Internet]. 2021 May 1 [cited 2024 Jan 11];10(5):1418. Available from: /pmc/articles/PMC8192987/
8. Hermelijn SM, Zwartjes RR, Tiddens HAWM, Cochius-Den Otter SCM, Reiss IKM, Wijnen RMH, et al. Associated Anomalies in Congenital Lung Abnormalities: A 20-Year Experience. Neonatology [Internet]. 2020 Feb 1 [cited 2024 Jan 12];117(6):697–703. Available from: https://pubmed.ncbi.nlm.nih.gov/32841951/
9. Scamporlino A, Ambrosini A, Turrini E, Morandi U, Stefani A. Congenital cystic adenomatoid malformation in adults, presenting as a single cyst. https://doi.org/101177/0218492318776572 [Internet]. 2018 May 2 [cited 2024 Jan 12];26(5):407–9. Available from:
https://journals.sagepub.com/doi/10.1177/0218492318776572?url_ver=Z39.88-2003&rfr_id=ori%3Arid%3Acrossref.org&rfr_dat=cr_pub++0pubmed
10. Patz EF, Müller NL, Swensen SJ, Dodd LG. Congenital cystic adenomatoid malformation in adults: CT findings. J Comput Assist Tomogr [Internet]. 1995 [cited 2024 Jan 11];19(3):361–4. Available from:
https://pubmed.ncbi.nlm.nih.gov/7790542/
11. Zeng Z, Liu C, Liu C, Pu Q, Mei J, Liao H, et al. Clinical characteristics and surgical treatment of congenital cystic adenomatoid malformation in adults: the largest cohort of 46 patients. Ann Transl Med [Internet]. 2022 May [cited 2024 Jan 11];10(10):596–596. Available from:
https://pubmed.ncbi.nlm.nih.gov/35722391/
12. Hartman GE, Shochat SJ. Primary pulmonary neoplasms of childhood: a review. Ann Thorac Surg [Internet]. 1983 [cited 2024 Jan 12];36(1):108–19. Available from:
https://pubmed.ncbi.nlm.nih.gov/6344822/
13. K Y CH’IN, M Y TANG. Arch Pathol (Chic). Sep;48(3):221-9. 1949 [cited 2024 Jan 11]. Congenital adenomatoid malformation of one lobe of a lung with general anasarca. Available from:
https://pubmed.ncbi.nlm.nih.gov/18137795/
14. Stocker JT, Madewell JE, Drake RM. Congenital cystic adenomatoid malformation of the lung. Classification and morphologic spectrum. Hum Pathol [Internet]. 1977 [cited 2024 Jan 11];8(2):155–71. Available from:
https://pubmed.ncbi.nlm.nih.gov/856714/
15. Stocker J.T. Congenital pulmonary airway malformation : a new name and expanded classification of congenital cystic adenomatoid malformation of the lung. Histopathology [Internet]. 2002 [cited 2024 Jan 11];41(2):424–31. Available from:
https://cir.nii.ac.jp/crid/1574231874759255680
16. Scott Adzick N, Harrison MR, Glick PL, Golbus MS, Anderson RL, Mahony BS, et al. Fetal cystic adenomatoid malformation: prenatal diagnosis and natural history. J Pediatr Surg [Internet]. 1985 [cited 2024 Jan 12];20(5):483–8. Available from:
https://pubmed.ncbi.nlm.nih.gov/3903097/
17. Gorospe L, Muñoz-Molina GM, Ayala-Carbonero AM, Fernández-Méndez MÁ, Arribas-Marcos Á, Castro-Acosta P, et al. Cystic adenomatoid malformation of the lung in adult patients: clinicoradiological features and management. Clin Imaging [Internet]. 2016 May 1 [cited 2024 Jan 14];40(3):517–22. Available from: https://pubmed.ncbi.nlm.nih.gov/27133697/
Publicado
2024-02-21
Cómo citar
Salinas Herrera, C. D., & Rodriguez Núñez , C. M. (2024). Malformación Congénita De La Vía Aérea Pulmonar Del Adulto Asociada A Persistencia De Ductus Arterioso . Ciencia Latina Revista Científica Multidisciplinar, 7(6), 8842-8850. https://doi.org/10.37811/cl_rcm.v8i1.9756
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Derechos de autor 2024 Cynthia Daniela Salinas Herrera, Christian Manuel Rodriguez Núñez
Esta obra está bajo licencia internacional Creative Commons Reconocimiento 4.0.
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